The Cystic Fibrosis Foundation has developed consensus recommendations for delivering palliative care to individuals with cystic fibrosis. These evidence-informed guidelines address primary and specialty palliative care models, screening for palliative needs, and strategies to improve quality of life across all stages of illness.
Newborn screening for cystic fibrosis (CF) has become a widely accepted and endorsed public health strategy in economically developed countries, although there is little consensus on optimal screening methods and gene panels.
The past six decades have seen remarkable improvements in health outcomes for people with cystic fibrosis, which was once a fatal disease of infants and young children. However, although life expectancy for people with cystic fibrosis...
The Cystic Fibrosis Foundation presents seven evidence-based recommendations to improve newborn screening for cystic fibrosis in the United States. These guidelines aim to enhance sensitivity, equity, and timeliness by refining IRT cutoff strategies, expanding CFTR variant panels, and improving communication with care teams.
This review highlights the importance of preventing malnutrition in cystic fibrosis (CF) patients, discussing recent findings on nutrition, the role of specific nutrients, exercise, and novel treatments like CFTR modulators.
The spectrum of conditions caused by abnormal CFTR function is broad – from ‘classic’ cystic fibrosis (CF) to single organ conditions termed CFTR-related disorders.
The Cystic Fibrosis Foundation has released evidence-based guidelines for managing CRMS/CFSPID, a designation for infants with inconclusive cystic fibrosis screening results. Developed by a multidisciplinary panel, the recommendations address genetic testing, monitoring, treatment, and communication strategies, with an emphasis on shared decision-making and minimizing unnecessary interventions.
Cystic fibrosis (CF) is an inherited genetic disorder with multiorgan involvement. Gastrointestinal tract dysfunction leads to fat and fat-soluble vitamins (A,D,E,K) malabsorption and deficiency of these vitamins.
Physical activity (PA) is important in the management of Cystic Fibrosis (CF) and is associated with a number of beneficial effects. PA assessment is not commonplace or consistent in clinical practice...
Objective: Cystic fibrosis diagnosis is dependent on the chloride ion concentration in the sweat test (≥60mEq/mL - recognized as the gold standard indicator for cystic fibrosis diagnosis).